Dentinogénesis imperfecta tipo IIReporte de caso de dos pacientes de un mismo grupo familiar

  1. María Eleonor Vélez León 1
  2. María José Fernández Siguencia 2
  1. 1 Universidad Católica de Cuenca
    info

    Universidad Católica de Cuenca

    Cuenca, Ecuador

    ROR https://ror.org/0036b6n81

  2. 2 Ministerio de Salud Pública del Ecuador
Journal:
Odontología Vital

ISSN: 2215-5740,  1659-0775

Year of publication: 2020

Volume: 2

Issue: 33

Pages: 21-28

Type: Article

DOI: 10.59334/ROV.V2I33.397 DIALNET GOOGLE SCHOLAR lock_openOpen access editor

More publications in: Odontología Vital

Sustainable development goals

Abstract

Introduction: Dentinogenesis imperfecta (DI) has been defined as a hereditary alteration of autosomal dominant character, which originates during the stage of histodifferentiation in dental development, is a type of dysplasia of dentinal tissue that affects the dentine structure of one or both dentitions. The complications of ID have a strong impact on the quality of life of patients since the functional, aesthetic and phonetic part are usually affected and represent an important challenge for the trafficker. Early diagnosis and adequate treatment are necessary to achieve better functional and aesthetic results, minimize nutritional deficiencies and psychosocial disorders, thus improving the quality of life of the person. Objective: To determine the type of dentinogenesis, the family relationship, and the clinical characteristics of each patient. Methods: Two brothers coming from the city of Cuenca-Ecuador, ages 5 and 6 years old, come to the Odontology clinic of the Catholic University of Cuenca, respectively, for presenting multiple carious lesions. Generalized destruction of the coronary remnant and premature loss of teeth. After performing the clinical and radiographic diagnosis, family history, the diagnosis of dentinogenesis imperfecta type II was established. Conclusion: the timely and early diagnosis of dentinogenesisimperfecta is of great importance for an adequate treatment, because the ID, affected mainly by the primary dentition, is fundamental visits to the dentist, since this will be able to diagnose the pathology at an early stage. Avoid big damages.

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